Hearing loss is the partial or complete loss of hearing in either one or both ears. This can occur suddenly in some cases, but typically it tends to develop gradually. Noise exposure accumulates over a lifetime, such that repeated exposure to loud noises increases the level of hearing loss experienced.…
Newborn hearing screening
What is newborn hearing screening?
Hearing screening is a tool used to identify hearing impairment, or hearing loss, in newborn babies and young children. A test that shows hearing impairment or unclear results is usually followed up with a detailed diagnostic assessment carried out by an audiologist.
Every baby is offered screening for hearing loss in the US. The sooner hearing loss is diagnosed, the better the outcomes. Hearing screening plays an important role in identifying and addressing hearing impairment because it can be difficult to tell if a baby has hearing loss during their first two months of life.
Hearing screening is non-invasive and is typically carried out by a nurse who has undergone specific training. Hearing screening can either be a single test, or a two-stage process. In two-stage screening, babies that show signs of hearing impairment in the initial test receive a second screening test. Only those showing a similar result in the second test are referred to an audiologist.
Hearing loss is classified by measuring the hearing threshold in decibels at various frequencies. Normal hearing has a threshold of 20 decibels (dB).
Hearing loss can be:
- Mild: 20-40dB;
- Moderate: 41-60dB;
- Severe: 61-90dB, and;
- Profound: more than 90dB.
Babies and young children identified as having moderate to profound hearing loss can receive support and early intervention to minimize the impact of their hearing impairment.
There are typically two tests that may be used to screen for hearing loss in newborns; an automated auditory brainstem response test, and otoacoustic emissions test. Screening typically takes place before the baby is discharged from hospital. The baby needs to be asleep or in a quiet and settled state during the screening test.
Automated auditory brainstem response test
This test measures the integrity of the inner ear and the auditory pathway. It can detect auditory neuropathy in children who are deaf, but who have normal otoacoustic emissions (as their cochlea is normal).
The stimulus is presented with either earphones or through an ear canal probe. Three specially-placed electrodes are used to detect the response from the brain stem. This is an automated device, so it can be performed by non-specialists. The test takes around 20 minutes to complete.
If the screening is not passed in one or both ears, the baby will undergo a second test, and may be referred to an audiologist for further assessment.
Otoacoustic emissions test
In a healthy cochlea, the hair cells vibrate in response to sound; this vibration generates acoustic energy, known as otoacoustic emissions.
This test measures the presence or absence of sound waves being generated by the hair cells on the cochlea in response to sound stimuli. A miniature microphone is placed in the outer ear canal and the microphone produces sounds stimuli and then detects sound waves generated by the cochlea.
If the screening test is not passed in one or both ears, the baby will undergo a second screening and may be referred to an audiologist for further assessment.
Hearing loss in newborns
Hearing is a critical part of a baby's cognitive, social and emotional development - a mild or partial hearing loss can affect their ability to speak and understand language. Young children with untreated hearing loss can experience delays in their language development, behavioral difficulties and underachieve at school.
It is estimated that around one in every 1000 babies is born with permanent hearing loss in both ears. The vast majority of deaf babies are born into families with normal hearing. 
For around half of all babies and young children with hearing loss, there is no associated cause.
Some possible causes of hearing loss in newborn babies may include:
- Infections during pregnancy;
- Certain medications used during pregnancy;
- Nervous system disorders;
- Being born prematurely;
- Genetic syndromes such as Usher, Down syndrome or Waardenburg syndrome;
- A family history of hearing loss, and;
- Complications during birth.
Some other factors that can cause 'acquired hearing loss' any time after birth include:
- Certain medications;
- A perforated eardrum;
- Untreated middle ear infections, and;
- A serious head injury.
Most babies who are diagnosed with some degree of hearing loss do not have any known risk factors, nor any underlying medical condition that is associated with hearing loss.
Babies with an increased risk of hearing loss include those with:
- A family history of childhood hearing loss;
- High levels of jaundice;
- Abnormalities of the head and neck;
- Congenital infections (HIV, toxoplasmosis, syphilis, varicella, rubella, cytomegalovirus);
- Admission to newborn intensive care unit;
- Meningitis or encephalitis;
- Aminoglycoside antibiotic therapy for more than three days;
- Low birth weight of less than 2,500 grams or 5 lbs. 8oz., and;
- The need for major cardiopulmonary resuscitation (CPR) at birth.
Babies at risk are typically offered repeat screening when they reach 9-12 months of age.
Newborn hearing loss can be:
- Conductive - caused by damage to the outer or middle ear;
- Sensorineural - caused by damage to the inner ear structures, or;
- Mixed - a combination of both.
Auditory neuropathy, one type of sensorineural hearing loss, is caused by absent or severely distorted auditory signals.
Conductive hearing loss is usually caused by abnormalities of the outer or middle ear, which limit the amount of external sound that can pass through to the inner ear. The function of the cochlea remains normal, because the inner, middle and outer ear develop separately.
Signs and symptoms
Although hearing screening tests can identify the majority of babies with mild or more severe hearing loss, it is still important to monitor a young child's speech and language developmental milestones to detect late onset or progressive types of hearing loss.
During the first year, babies learn how to hear and recognize the sounds of their parents' language. They may experiment with sounds by babbling, which progresses to them making real words.
Some of the more typical milestones a baby reaches in their first year of life include:
- Startling or jumping with a sudden, loud noise;
- By three months of age, recognizing a parent's voice;
- By six months of age, turning their head or eyes towards a sound, and;
- By 12 months of age, imitating some sounds and producing a few words such as 'mama' or 'bye'.
Babies and young children experience huge development in their speech sounds. By the age of two, around half of their speech can be understood, and by the age of three, most of their speech can be understood.
As the baby grows, some signs that may be associated with hearing impairment may include:
- Turning up the television volume excessively;
- Not replying when called;
- Having articulation problems with language and speech;
- Having difficulty understanding speech;
- Not being startled by sudden, loud noises;
- Poor academic performance;
- Being unable to determine where a sound is coming from, and;
- Speaking differently compared to other children their age.
Types of treatment
Early intervention services for newborn babies identified with a hearing impairment will enable improved speech, language and academic performance.
Hearing loss can:
- Impair the academic performance of children, and;
- Cause feelings of loneliness, isolation and frustration;
Adults with hearing loss can experience higher rates of unemployment.
Early intervention enables babies and young children to develop better language, speech and learning skills as their brain is exposed to language earlier. It is crucial for maximizing the potential speech and language development of babies with hearing loss.
Ways to help prevent hearing loss in babies and young children include:
- Newborn hearing screening. Australian Prescriber – an independent review. Accessed 6 November 6 2014, from http://www.australianprescriber.com/magazine/26/4/82/4/
FAQ Frequently asked questions
What are the symptoms of hearing loss?
A baby typically achieves certain milestones during their speech and language development. When a baby or infant appears to have missed some of these milestones, it may indicate they have hearing loss. Some of the more typical milestones may include a …
What causes congenital hearing loss?
Some of the more typical causes of congenital hearing loss include: infections during pregnancy; nervous system disorders; being born prematurely; a family history of hearing loss, and; complications during birth.
Who can develop hearing loss?
Around one in every 1000 births are affected by permanent bilateral hearing loss. Around half of babies born with or developing hearing loss do so with no previous risk factors.
How is hearing loss diagnosed?
In Australia, newborn babies are routinely screened to identify babies born with, or at risk of, developing hearing loss.
How is hearing loss treated?
Treatment of hearing loss varies depending on the cause and severity of hearing loss, and the age of the child, but early intervention measures may include hearing aids and support services.
Can hearing loss be prevented?
Hearing loss in newborns cannot be totally prevented, but there are things you can do to minimize the risk, including keeping childhood vaccinations up to date, and getting early treatment for ear infections.
Are there different types of hearing loss?
Hearing loss can be: conductive - caused by damage to the outer or middle ear; sensorineural - caused by damage to the inner ear structures, or; mixed - caused by a combination of both.
What increases the chances of developing hearing loss?
The following can increase the chance of developing hearing loss: 1) Congenital infections such as HIV, toxoplasmosis, syphilis, varicella, rubella, cytomegalovirus or herpes. 2) Hyperbilirubinemia (too much bilirubin in the blood). 3) …